Idiopathic Intracranial Hypertension with Multiple Cranial Nerve Involvement: A Clinical Enigma

  • Ankita Sheoran Postgraduate Resident, Department of Medicine, Dr. RML Hospital, New Delhi, India.
  • Renu Dabas Senior Resident, Department of Medicine, Dr. RML Hospital, New Delhi, India.
  • Ayush Malhotra Senior Resident, Department of Medicine, Dr. RML Hospital, New Delhi, India.
  • Pratap Singh Associate Professor, Department of Medicine, Dr. RML Hospital, New Delhi, India. https://orcid.org/0000-0001-6291-4287
Keywords: Cranial Nerve, CSF, IIH

Abstract

Idiopathic Intracranial Hypertension (IIH), previously known as Pseudotumor cerebri is characterized by raised intracranial pressure without any obvious reason. Early clinical suspicion and targeted investigations are crucial for early diagnosis and can prevent potential blindness. We hereby report this case of a young lady who presented with involvement of multiple cranial nerves, and responded dramatically to the treatment.

References

Boulton M, Armstrong D, Flessner M et al. Raised intracranial pressure increases CSF drainage through

arachnoid villi and extracranial lymphatics. Am J Physiol 1998; 275(3Pt2): 889-896.

Lee A, Wall M. Idiopathic intracranial hypertension (pseudotumor cerebri): epidemiology and pathogenesis.

Available from: http://www.uptodate.com/contents/idiopathic-intracranial-hypertension-pseudotumorcerebri-

epidemiology-and-pathogenesis. Accessed January 22, 2019.

Chen J, Wall M. Epidemiology and Risk Factors for Idiopathic Intracranial Hypertension. Int Ophthalmol

Clin 2014; 54(1): 1-11.

Friedman DI, Liu GT, Digre KB. Revised diagnostic criteria for the pseudotumor cerebri syndrome in adults and

children. Neurology 2013; 81(13): 1159-1165.

Degnan AJ, Levy LM. Pseudotumor cerebri: brief review of clinical syndrome and imaging findings. American Journal of Neuroradiology 2011; 32(11): 1986-1993.

Celebisoy N, Gokcay F, Sirin H et al. Treatment of idiopathic intracranial hypertension: topiramate vs

acetazolamide, an open-label study. Acta Neurol Scand 2007; 116: 322-327.

Kanagalingam S, Subramanian P. Cerebral venous sinus stenting for pseudotumor cerebri: a review. Saudi J

Ophthalmol 2015; 29(1): 3-8.

Published
2019-12-24