Fahr’s Syndrome: A Typical Entity Presenting as Psychosis

  • Prerak Kumar Senior Resident, Department of Psychiatry and Drug Deaddiction Centre, Lady Hardinge Medical College and S.K. Hospital, New Delhi, 110001. https://orcid.org/0000-0001-9256-3406
  • Prerna Kukreti Associate Professor, Department of Psychiatry and Drug Deaddiction Centre, Lady Hardinge Medical College and S.K. Hospital, New Delhi, India.
  • Saurabh Junior Resident, Department of Psychiatry and Drug Deaddiction Centre, Lady Hardinge Medical College and S.K. Hospital, New Delhi, India.
  • Harita Mathur Junior Resident, Department of Psychiatry and Drug Deaddiction Centre, Lady Hardinge Medical College and S.K. Hospital, New Delhi, India.
  • Komal Kohat Junior Resident, Department of Psychiatry and Drug Deaddiction Centre, Lady Hardinge Medical College and S.K. Hospital, New Delhi, India.
  • Dinesh Kataria Director Professor and Head, Department of Psychiatry and Drug Deaddiction Centre, Lady Hardinge Medical College and S.K. Hospital, New Delhi, India.
Keywords: Basal Ganglia Calcification, Fahr’s Syndrome, Parathyroid Hormone, Hypocalcemia, Psychiatric Symptoms

Abstract

Fahr’s syndrome is a rare neurological entity characterized by bilateral and symmetrical intracranial deposition of calcium mainly in the basal ganglia. Motor and Psychiatric symptoms are clinically relevant features in this syndrome. We report a case where psychiatric symptoms and features of delirium were more prominent as compared to motor symptoms. Radiological findings depicted bilateral basal ganglia calcification and oedema in parietal region mainly on right side. Parathyroid hormone and calcium levels were mildly low with no significant past or family history. Most behavioural symptoms showed significant improvement on treatment with Risperidone, Amisulpride, Lorazepam, Sodium Valproate, Calcium, Folic acid and Trihexyphenidyl but some symptoms like auditory hallucinations remained unresponsive.

How to cite this article:
Kumar P, Kukreti P, Mathur H, Saurabh, Kohat K, Kataria D. Fahr’s Syndrome: A Typical Entity Presenting as Psychosis. J Adv Res Psychol Psychother 2020; 3(1): 29-31.

DOI: https://doi.org/10.24321/2581.5822.202006

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Published
2020-05-15